Congenital Heart Disease Post Test

A neonate alerted in cyanotic with reduced GCS and signs of shock. Initial assessment reveals absent femoral pulses, delayed capillary refill time and hypotension. A Prostaglandin infusion is started which initially improves symptoms for further assessment to take place. The following image is the child’s chest X-ray.

What is the most likely diagnosis?

Which of the following is a common side effect of Prostaglandin infusions to be aware of?

A concerned mother attended ED with her child. Following her 6 week baby check, she noted that the GP mentioned a heart murmur. The child is well with a normal examination. There is a continuous systolic murmur.

What is the most likely lesion?

Which of the following lesions are incompatible with life if there is no shunt present?  (VSD/ASD/PDA)

A 5-day-old neonate is brought in collapsed and severely cyanosed. You call a paediatric anaesthetist and prepare to assess. Cyanosis improves following initiation of a prostaglandin infusion. The following is the infants X-ray.

What is the cause of cyanosis?

Which of the following lesions can cause absent or delayed femoral pulses to be present on examination?

True or false: Supracardiac and Infracardiac TAPVD present later in life as there is less obstruction to pulmonary flow, therefore, CCF and cyanosis occur later.

Which of the following lesions cause shunting of blood from the right to the left side of the heart and therefore lead to cyanosis?

True or false: A BT  shunt or Conduit from the Pulmonary Artery to the Right Atrium can be used in duct dependent lesions to maintain adequate blood flow.

Which of the following is the final procedure used in the staged repair of Hypoplastic Left Heart Syndrome?